Papers - KATSUNO, Masahisa
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Silencing neuronal mutant androgen receptor in a mouse model of spinal and bulbar muscular atrophy. Reviewed
Sahashi K, Katsuno M, Hung G, Adachi H, Kondo N, Nakatsuji H, Tohnai G, Iida M, Bennett CF, Sobue G.
Hum Mol Genet. Vol. 24 ( 21 ) page: 5985-5994 2015
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FUS regulates AMPA receptor function and FTLD/ALS-associated behaviour via GluA1 mRNA stabilization. Reviewed
Udagawa T, Fujioka Y, Tanaka M, Honda D, Yokoi S, Riku Y, Ibi D, Nagai T, Yamada K, Watanabe H, Katsuno M, Inada T, Ohno K, Sokabe M, Okado H, Ishigaki S, Sobue G.
Nat Commun. Vol. 6 page: 7098 2015
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Astrocyte-Derived TGF-β1 Accelerates Disease Progression in ALS Mice by Interfering with the Neuroprotective Functions of Microglia and T Cells. Reviewed
Endo F, Komine O, Fujimori-Tonou N, Katsuno M, Jin S, Watanabe S, Sobue G, Dezawa M, Wyss-Coray T, Yamanaka K.
Vol. 11 ( 4 ) page: 592-604 2015
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Pioglitazone suppresses neuronal and muscular degeneration caused by polyglutamine-expanded androgen receptors. Reviewed
Iida M, Katsuno M, Nakatsuji H, Adachi H, Kondo N, Miyazaki Y, Tohnai G, Ikenaka K, Watanabe H, Yamamoto M, Kishida K, Sobue G.
Hum Mol Genet. Vol. 24 ( 2 ) page: 314-329 2015
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Tongue pressure as a novel biomarker of spinal and bulbar muscular atrophy (SBMA). Reviewed
Mano T, Katsuno M, Banno H, Suzuki K, Suga N, Hashizume A, Araki A, Watanabe H, Tanaka S, Yamamoto M, Sobue G
Vol. 82 page: 255-262 2014
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Brugada syndrome in spinal and bulbar muscular atrophy. Reviewed
Araki A, Katsuno M, Suzuki K, Banno H, Suga N, Hashizume A, Mano T, Hijikata Y, Nakatsuji H, Watanabe H, Yamamoto M, Makiyama T, Ohno S, Fukuyama M, Morimoto S, Horie M, Sobue G.
Neurology Vol. 82 page: 1813-1821 2014
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Paeoniflorin eliminates a mutant AR via NF-YA-dependent proteolysis in spinal and bulbar muscular atrophy. Reviewed
Tohnai G, Adachi H, Katsuno M, Doi H, Matsumoto S, Kondo N, Miyatzaki Y, Iida M, Nakatsuji H, Qiang Q, Ding Y, Watanabe H, Yamamoo M, Ohtsuka K, Sobue G.
Hum Mol Genet Vol. 23 page: 3552-3565 2014
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Schwann cell involvement in the peripheral neuropathy of spinocerebellar ataxia type 3. Reviewed
Suga N, Katsuno M, Koike H, Banno H, Suzuki K, Hashizume A, Mano T, Iijima M, Kawagashira Y, Hirayama M, Nakamura T, Watanabe H, Tanaka F, Sobue G.
Neuropathol Appl Neurobiol. Vol. 40 page: 628-639 2014
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Heat shock factor-1 influences pathological lesion distribution of polyglutamine-induced neurodegeneration. Reviewed
Kondo N, Katsuno M, Adachi H, Minamiyama M, Doi H, Matsumoto S, Miyazaki Y, Iida M, Tohnai G, Nakatsuji H, Ishigaki S, Fujioka Y, Watanabe H, Tanaka F, Nakai A, Sobue G.
Nat Commun Vol. 4 page: 1405 2013
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Amyotrophic lateral sclerosis: an update on recent genetic insights. Invited Reviewed
Iguchi Y, Katsuno M, Ikenaka K, Ishigaki S, Sobue G
J Neurol Vol. 260 page: 2917-2927 2013
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FUS-regulated region- and cell-type-specific transcriptome is associated with cell selectivity in ALS/FTLD. Reviewed
Fujioka Y, Ishigaki S, Masuda A, Iguchi Y, Udagawa T, Watanabe H, Katsuno M, Ohno K, Sobue G
Sci Rep Vol. 3 page: 2388 2013
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RNP2 of RNA Recognition Motif 1 Plays a Central Role in the Aberrant Modification of TDP-43. Reviewed
Takagi S, Iguchi Y, Katsuno M, Ishigaki S, Ikenaka K, Fujioka Y, Honda D, Niwa J, Tanaka F, Watanabe H, Adachi H, Sobue G
Vol. 8 page: e66966 2013
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A functional deficiency of TERA/VCP/p97 contributes to impaired DNA repair in multiple polyglutamine diseases. Reviewed
Fujita K, Nakamura Y, Oka T, Ito H, Tamura T, Tagawa K, Sasabe T, Katsuta A, Motoki K, Shiwaku H, Sone M, Yoshida C, Katsuno M, Eishi Y, Murata M, Paul Taylor J, Wanker EE, Kono K, Tashiro S, Sobue G, La Spada AR, Okazawa H
Vol. 4 page: 1816 2013
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p62/SQSTM1 Differentially Removes the Toxic Mutant Androgen Receptor via Autophagy and Inclusion Formation in a Spinal and Bulbar Muscular Atrophy Mouse Model. Reviewed
Doi H, Adachi H, Katsuno M, Minamiyama M, Matsumoto S, Kondo N, Miyazaki Y, Iida M, Tohnai G, Qiang Q, Tanaka F, Yanagawa T, Warabi E, Ishii T, Sobue G
Vol. 33 page: 7710-7727 2013
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Loss of TDP-43 causes age-dependent progressive motor neuron degeneration. Reviewed
Iguchi Y, Katsuno M, Niwa JI, Takagi S, Ishigaki S, Ikenaka K, Kawai K, Watanabe H, Yamanaka K, Takahashi R, Misawa H, Sasaki S, Tanaka F, Sobue G
Brain Vol. 136 page: 1371-1382 2013
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Translational research on disease-modifying therapies for neurodegenerative diseases. Invited Reviewed
Katsuno M, Watanabe H, Tanaka F, Sobue G
Neurology and Clinical Neuroscience Vol. 1 page: 3-10 2013
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dnc-1/dynactin 1 knockdown disrupts transport of autophagosomes and induces motor neuron degeneration. Reviewed
Ikenaka K, Kawai K, Katsuno M, Huang Z, Jiang YM, Iguchi Y, Kobayashi K, Kimata T, Waza M, Tanaka F, Mori I, Sobue G
PLoS One Vol. 8 page: e54511 2013
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Cortical and subcortical brain atrophy in Parkinson's disease with visual hallucination. Reviewed
Watanabe H, Senda J, Kato S, Ito M, Atsuta N, Hara K, Tsuboi T, Katsuno M, Nakamura T, Hirayama M, Adachi H, Naganawa S, Sobue G.
Mov Disord Vol. 28 page: 1732-1736 2013
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c-Abl inhibition delays motor neuron degeneration in the G93A mouse, an animal model of amyotrophic lateral sclerosis. Reviewed
Katsumata R, Ishigaki S, Katsuno M, Kawai K, Sone J, Huang Z, Adachi H, Tanaka F, Urano F, Sobue G.
PLoS One Vol. 7 page: e46185 2012
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Naratriptan mitigates CGRP1-associated motor neuron degeneration caused by expanded polyglutamine. Reviewed
Minamiyama M, Katsuno M, Adachi H, Doi H, Kondo N, Iida M, Ishigaki S, Fujioka Y, Matsumoto S, Miyazaki Y, Tanaka F, Kurihara H, Sobue G.
Nat Med. Vol. 18 page: 1531-1538 2012